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Archive for the ‘Rare Diseases’ Category

What is Hodgkin’s disease in adults?

Crohn’s (disease) in adults is a so-called Hodgkin’s lymphoma. This form of cancer affects the lymph glands, so a part of the body’s defense system (immune system).

The lymphatic system branches out of thin tubes – like blood – throughout the entire body. Lymph vessels carry lymph, a colorless, watery fluid, called lymphocytes, which belong to the white blood cell contains. Along the lymphatic vessels are small bean-shaped organs called lymph nodes. Groups of lymph nodes are located in the underarm, pelvis, neck and abdomen. The lymph nodes produce and store cells that fight infection in the body. The spleen (an organ in the upper abdomen that produces lymphocytes and filters out old blood cells), the thymus gland (a small organ beneath the breastbone) and the tonsils are part of the lymphatic system.

Because lymph tissue throughout the body is a Hodgkin can emerge anywhere in the body. It can affect almost all organs of the body, including the liver and bone marrow (the spongy tissue in the bone structure, which produces blood cells) and the spleen. Read the rest of this entry »

Summary
Progeria syndrome or Hutchinson-Gilford syndrome is a rare. Consists of the signs of aging in children between their first and second year of life.The differential diagnosis of this entity should be considered with any other progeroid syndromes described in the literature. We present an updated review on the subject with emphasis on diagnostic box.
(Keywords: progeria, Hutchinson-Gilford syndrome, inheritance, progeroid syndromes.)

Hutchinson-Gilford syndrome
The Hutchinson-Gilford progeria syndrome is an Uncommon or disease. Its Clinical Manifestations Are Evident by the first or second year of life and Are Characterized by a general appearance of premature aging. Most Cases Are Sporadic and an autosomal dominant inheritance Arising Has Been Suggested by a de novo mutation. It Should Be Considered in the differential diagnosis of premature aging, Along With Other syndromes Described in the literature. We present a review of progeria with special emphasis on diagnostic methods. Read the rest of this entry »